Background: Limb-girdle muscular dystrophies (LGMDs) belong to few neuromuscular disorders mainly involving\npelvic and shoulder girdle muscles. Also, cardiac or pulmonary complications, increased rhabdomyolysis risk when\nexposed to volatile anesthetics and succinylcholine may increase anesthesia related risks. However, current reports\nabout the anesthesia management of these patients are limited.\nCase presentation: We described our anesthetic management of a 36 years old woman with LGMD 2B receiving\narthroscopic knee surgery. In consideration of the high risk of rhabdomyolysis, total intravenous anesthesia (TIVA)\nwas selected for her surgery. Considering the unpredictable respiratory depression, opioid based patient-controlled\nintravenous analgesia was replaced with an intra-articular cocktail therapy consisting of 20 ml of 0.2% ropivacaine.\nAlso, we reviewed the literatures on anesthetic management of LGMD through searching PubMed, in order to\nprovide a comprehensive and safe guidance for the surgery.\nConclusions: Carefully conducted general anesthesia with TIVA technique is a good choice for LGMD patients.\nNeuraxial anesthesia may be used if general anesthesia needs to be avoided. To warrant safe anesthesia for surgery,\nany decision must be well thought out during perioperative period.
Loading....